Ruptura no traumática del bazo como forma de presentación de la amilosis AL en un paciente joven.

Autores/as

  • Yasmine Smadhi Maouche Service de Medecine Polyvalente. Centre Hospitalier de Creil. Francia
  • Mounir Ouali Service de Chirurgie Digestive. Centre Hospitalier de Creil. Francia
  • Fahima Belhoul Service de Chirurgie Digestive. Centre Hospitalier de Creil. Francia
  • Renato Demontis Service de Néphrologie. Centre Hospitalier de Creil. Francia
  • Sai Atmani Service d’Hématologie. Centre Hospitalier de Creil. Francia
  • Tahar Benali Service de Cardiologie. Centre Hospitalier de Creil. Francia
  • Noel Lorenzo-Villalba Service de Médecine Interne, Diabète et Maladies Métaboliques. Hôpitaux Universitaires de Strasbourg

Palabras clave:

Amyloidosis, Proteinuria, Splenic Rupture

Resumen

We report a 35-year-old sportive man who was admitted to the emergency department for worsening of acute spontaneous abdominal pain appearing at rest. He only referred having lifted a tree trunk the day before, but he was used to perform such physical efforts. The clinical course at the emergency department was marked by the development of severe anemia secondary to a progressive splenic hematoma and acute pulmonary distress. The patient benefited from total splenectomy. Laboratory data showed hypogammaglobulinemia, proteinuria and the anatomopathological examinations of both spleen and kidneys were consistent with light chain amyloidosis.

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Publicado

2022-08-02

Cómo citar

Smadhi Maouche, Y., Ouali, M., Belhoul, F., Demontis, R., Atmani, S., Benali, T., & Lorenzo-Villalba, N. (2022). Ruptura no traumática del bazo como forma de presentación de la amilosis AL en un paciente joven. Revista Médica De Chile, 150(5). Recuperado a partir de https://mail.revistamedicadechile.cl/index.php/rmedica/article/view/9535

Número

Sección

Reporte de Caso Clínico